Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia
نویسندگان
چکیده
Hereditary Haemorrhagic Telangiectasia (HHT) is an autosomal dominant disorder characterized by vascular dysplasia. Hepatic Vascular Malformations (VMs) range from small telangiectases to significant shunting. Here we report two cases of HHT. Case 1 had diffuse ectasia the hepatic artery along its intrahepatic and extrahepatic course with a arterial aneurysm. 2 presented ileal telangiectases. Knowledge these variants indispensable for clinicians radiologists in aiding diagnosis surgical interventional management.
 Keywords: Malformations, HHT, Arteriovenous Malformation, Ileal Telangiectasis.
منابع مشابه
Hereditary haemorrhagic telangiectasia.
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ژورنال
عنوان ژورنال: Sultan Qaboos University Medical Journal
سال: 2023
ISSN: ['2075-0528', '2075-051X']
DOI: https://doi.org/10.18295/squmj.1.2023.011